E-ISSN 2534-9821
 

Case Report 


Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome

Yeliz Kılıç, Murat Vural, Mehmet Sacit Güleç.

Abstract
Background: Emanuel syndrome (ES) is a rare hereditary disorder characterized by growth and mental retardation, congenital malformations, and craniofacial anomalies. There is limited data on the anesthetic management of this syndrome, all of which come from case reports. Report: A 7-year-old girl presented with urinary incontinence caused by tethered cord syndrome. Laminoplasty plus transection of the tight filum terminale to release the tethered conus medullaris under total intravenous anesthesia was performed. Discussion: Anesthesia management of patients with ES requires special attention due to the airway difficulties associated with micrognathia and palate anomalies and accompanying congenital malformations that primarily affect cardiovascular and neurologic systems. Monitoring the cardiac parameters and neurological signs during the surgery is of great importance for the patient safety. Conclusion: This case report is the first demonstrating total intravenous anesthesia in patients with ES, and may help to guide anesthesiologists in the anesthetic management of these patients.

Key words: Airway management, total intravenous anesthesia, difficult intubation, Emanuel syndrome


 
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How to Cite this Article
Pubmed Style

Kilic Y, Vural M, Gulec MS. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. Int J Med Rev Case Rep. 2020; 4(12): 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child


Web Style

Kilic Y, Vural M, Gulec MS. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. http://www.mdpub.net/?mno=21440 [Access: January 31, 2021]. doi:10.5455/IJMRCR.tethered-cord-syndrome-child


AMA (American Medical Association) Style

Kilic Y, Vural M, Gulec MS. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. Int J Med Rev Case Rep. 2020; 4(12): 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



Vancouver/ICMJE Style

Kilic Y, Vural M, Gulec MS. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. Int J Med Rev Case Rep. (2020), [cited January 31, 2021]; 4(12): 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



Harvard Style

Kilic, Y., Vural, . M. & Gulec, . M. S. (2020) Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. Int J Med Rev Case Rep, 4 (12), 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



Turabian Style

Kilic, Yeliz, Murat Vural, and Mehmet Sacit Gulec. 2020. Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. International Journal of Medical Reviews and Case Reports, 4 (12), 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



Chicago Style

Kilic, Yeliz, Murat Vural, and Mehmet Sacit Gulec. "Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome." International Journal of Medical Reviews and Case Reports 4 (2020), 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



MLA (The Modern Language Association) Style

Kilic, Yeliz, Murat Vural, and Mehmet Sacit Gulec. "Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome." International Journal of Medical Reviews and Case Reports 4.12 (2020), 46-47. Print. doi:10.5455/IJMRCR.tethered-cord-syndrome-child



APA (American Psychological Association) Style

Kilic, Y., Vural, . M. & Gulec, . M. S. (2020) Anesthetic management for tethered cord syndrome in a child with Emanuel syndrome. International Journal of Medical Reviews and Case Reports, 4 (12), 46-47. doi:10.5455/IJMRCR.tethered-cord-syndrome-child