E-ISSN 2534-9821
 

Case Report

Online Publishing Date:
13 / 10 / 2020

 


Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap

Shania Niromi Gunasekera, Harindra Karunathilaka, Verni Sopan, Priyanka Yogananda, Ananda Jayanaga.


Abstract
Polymyositis is an autoimmune myopathy with a preponderance to involve proximal limb muscles in a symmetrical manner. Type two respiratory failure and severe bulbar weakness is not a common mode of initial presentation of polymyositis – systemic sclerosis overlap syndrome. We present a case of a middle age female , who presented with dysphagia, nasal regurgitation, aspiration of food and proximal muscle weakness, worsening over 6 months duration. The disease was rapidly progressing and culminated in severe respiratory muscle weakness and respiratory arrest necessitating invasive ventilation. The diagnosis of sero- negative polymyositis and systemic sclerosis overlap syndrome was made and she achieved a remarkable recovery with intensive care and meticulous immunosuppressive therapy.
Physicians should be aware of the rapid respiratory muscle involvement in systemic sclerosis and Polymyositis overlap since timely initiation of treatment is life saving.

Key words: Polymyositis, Systemic sclerosis, overlap syndrome, respiratory failure, proximal myopathy


 
ARTICLE TOOLS
Abstract
PDF Fulltext
How to cite this articleHow to cite this article
Citation Tools
Related Records
 Articles by Shania Niromi Gunasekera
Articles by Harindra Karunathilaka
Articles by Verni Sopan
Articles by Priyanka Yogananda
Articles by Ananda Jayanaga
on Google
on Google Scholar


How to Cite this Article
Pubmed Style

Gunasekera SN, Karunathilaka H, Sopan V, Yogananda P, Jayanaga A. Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap. Int J Med Rev Case Rep. 2020; 4(12): 61-63. doi:10.5455/IJMRCR.2020-05-203


Web Style

Gunasekera SN, Karunathilaka H, Sopan V, Yogananda P, Jayanaga A. Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap. https://www.mdpub.net/?mno=111167 [Access: April 05, 2024]. doi:10.5455/IJMRCR.2020-05-203


AMA (American Medical Association) Style

Gunasekera SN, Karunathilaka H, Sopan V, Yogananda P, Jayanaga A. Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap. Int J Med Rev Case Rep. 2020; 4(12): 61-63. doi:10.5455/IJMRCR.2020-05-203



Vancouver/ICMJE Style

Gunasekera SN, Karunathilaka H, Sopan V, Yogananda P, Jayanaga A. Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap. Int J Med Rev Case Rep. (2020), [cited April 05, 2024]; 4(12): 61-63. doi:10.5455/IJMRCR.2020-05-203



Harvard Style

Gunasekera, S. N., Karunathilaka, . H., Sopan, . V., Yogananda, . P. & Jayanaga, . A. (2020) Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap. Int J Med Rev Case Rep, 4 (12), 61-63. doi:10.5455/IJMRCR.2020-05-203



Turabian Style

Gunasekera, Shania Niromi, Harindra Karunathilaka, Verni Sopan, Priyanka Yogananda, and Ananda Jayanaga. 2020. Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap. International Journal of Medical Reviews and Case Reports, 4 (12), 61-63. doi:10.5455/IJMRCR.2020-05-203



Chicago Style

Gunasekera, Shania Niromi, Harindra Karunathilaka, Verni Sopan, Priyanka Yogananda, and Ananda Jayanaga. "Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap." International Journal of Medical Reviews and Case Reports 4 (2020), 61-63. doi:10.5455/IJMRCR.2020-05-203



MLA (The Modern Language Association) Style

Gunasekera, Shania Niromi, Harindra Karunathilaka, Verni Sopan, Priyanka Yogananda, and Ananda Jayanaga. "Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap." International Journal of Medical Reviews and Case Reports 4.12 (2020), 61-63. Print. doi:10.5455/IJMRCR.2020-05-203



APA (American Psychological Association) Style

Gunasekera, S. N., Karunathilaka, . H., Sopan, . V., Yogananda, . P. & Jayanaga, . A. (2020) Early respiratory involvement leading to respiratory failure in a case of Systemic sclerosis – Polymyositis overlap. International Journal of Medical Reviews and Case Reports, 4 (12), 61-63. doi:10.5455/IJMRCR.2020-05-203